BRUGADA SYNDROME-A CASE REPORT

Kuzevska-Maneva Konstandina, Kacarska Rozana, Gjurkova-Angelovska Beti, Georgiev Antonio

Abstract


 

Brugada syndrome is a type of arrhythmia disorder, which is characterised by abnormal electrocardiogram (ECG) findings and an increased risk of sudden cardiac death. The most frequent sign is a persistent ST elevation in the electrocardiographic leads V1-V3 with a right bundle branch block (RBBB).We present a case of 12 years old healthy child, without any complains until then.  He had 2 episodes of collapse/syncope, which lasted long and spontaneously disappeared. The collapses were provoked by physical activity. On ECG we found sinus rhythm 62 bpm, RBBB (right bundle brunch block) and Brugada signs in V2 and V3 channel-ST elevation ≥ 2mm. The child was sent in electrophysiological centre abroad where the electrophysiological study was performed. They did not found any accessory pathway. The atrioventricular (AV) conduction was normal. Long lasting polymorphic ventricular tachycardia/fibrillation was induced with programed stimulation with 3 extrastimuli in right ventricular outflow tract. Performing one defibrillation the rhythm turned in sinus way. Then they performed ECG with translocation of electrodes V1-3 in 2nd intercostal space and the Brugada I type findings was discovered. After confirming of presence of Brugada type -1 syndrome the implantable cardioverter- defibrillator (ICD) was applied on child heart.

 

Key words: Brugada syndrome, ventricular fibrillation, sudden cardiac death



Keywords


Key words: Brugada syndrome, ventricular fibrilation, sudden cardiac death

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References


Brugada J, Brugada P, Brugada R. The syndrome of right bundle branch block ST segment elevation in V1 to V3 and sudden death--the Brugada syndrome. Europace. 1999;1(3): 156–66.

Brugada P, Brugada J, Roy D. Brugada syndrome 1992-2012: 20 years of scientific exitement, and more. Eur Heart J. 2013;34(47):3610-5.

Conte G, Sieira J, Ciconte G, et al. Reply: Early Repolarisation: A Risk Factor in Brugada Syndrome. J Am Coll Cardiol. 2015; 66(2):206-7.

Benito B, Sarcozy A, Mont L, et al. Gendre Differences in Clinical Manifetsation of Brugada Syndrome. J Am Coll Cardiol. 2008; 52(19):1567-73.

Patel SS, Anees S, Ferrick KJ. Prevalence of a Brugada pattern electrocardiogram in an urban population in the United States. Pacing Clin Electrophysiol. 2009; 32(6):704–8.

Sidik NP, Quay CN, Loh FC , Chen LY. Prevalence of Brugada sign and syndrome in patients presenting with arrhythmic symptoms at a Heart Rhythm Clinic in Singapore. Europace. 2009; 11(5):650–6.

Wajed A, Aslam Z, Abbas SF, et al. Frequency of Brugada-type ECG pattern (Brugada sign) in an apparently healthy young population. J Ayub Med Coll Abbottabad. 2008; 20(3):121–4.

Antzelevitch C, Brugada P, Borggrefe M, et al. Brugada syndrome. Report of the second consensus conference approaches to tachyarrhythmias. Hearth Rhythm. 2005; 2(4):429-40.

Take Y, Morita H, Toh N, et al. Identification of high-risk syncope related to ventricular fibrillation in patients with Brugada syndrome. Heart Rhythm. 2012;9(5):752-9.

Raju H, Papadakis M, Govindan M, et al. Low prevalence of risk markers in cases of sudden death due to brugada syndrome relevance to risk stratification in brugada syndrome. J Am Coll Cardiol. 2011; 57(23):2340-5.

Mizusawa Y,Wilde AA. Brugada syndrome. Circ Arrhythm and Electrophysiol. 2012;5(3):606-16.

Sheikh AS, Ranjan K. Brugada syndrome: a review of the literature. Clin Med. 2014;14(5):482-9.

Kapplinger JD, Tester DJ, Alders M et al. An international compendium of mutations in the SCN5A-encoded cardiac sodium channel in patients referred for Brugada syndrome genetic testing. Heart Rhythm. 2010; 7(1):33-46.

Zipes DP, Jalife J, eds. Cardiac Electrophysiology: From Cell to Bedside. 6th ed. Philadelphia: Saunders Elsevier; 2014.




DOI: http://dx.doi.org/10.24125/sanamed.v11i1.84

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